Diagnosis and management of prune belly syndrome in pediatric patients

Shirley Cecibel Zamora Núñez; Elizabeth Cristina Mayorga Aldaz; María de Lourdes Llerena Cepeda

doi:10.59471/ijhsc202473

Authors

Shirley Cecibel Zamora Núñez Universidad Regional Autónoma de Los Andes, Matriz Ambato, Ecuador. Author https://orcid.org/0009-0004-5013-2826
Elizabeth Cristina Mayorga Aldaz Universidad Regional Autónoma de Los Andes, Matriz Ambato, Ecuador. Author https://orcid.org/0000-0002-6441-2819
María de Lourdes Llerena Cepeda Universidad Regional Autónoma de Los Andes, Matriz Ambato, Ecuador. Author https://orcid.org/0000-0001-6112-3627

DOI:

https://doi.org/10.59471/ijhsc202473

Keywords:

Prune Belly Syndrome, cryptorchidism, urological abnormalities, diagnosis, treatment

Abstract

Prune-Belly Syndrome has been defined as a rare urological congenital anomaly. Worldwide, a prevalence of 1 per 50,000 live births was described. Among the characteristics that identify this syndrome are the deficiency of the abdominal wall musculature, dilation of the urinary tract and bilateral cryptorchidism. Management requires great interdisciplinary knowledge and even urological surgery. The objective of this work was to identify the main methods of diagnosis and management of Prune Belly Syndrome in pediatric patients through a bibliographic review. The bibliographic review was carried out with articles published from 2017 to 2023 in high-impact journals, 25 articles were found, 8 had case reports and 17 were a theoretical source of information. In short, the key diagnosis is established by means of a prenatal ultrasound, with respect to management it can be conservative or surgical and multidisciplinary management with specialists is important.

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